Neurology Medicine

Photo cameral SLK is a rare syndrome that occurs most often in boys than in girls. The onset occurs between 18 months and 13 years and three quarters of cases have their onset before age 7 for children, otherwise previously normal. In some cases, language development may have been somewhat delayed, however, is a clear regression constant verbal skills acquired previously.

The typical profile is: normal development and appropriate language in the first 3-7 years, loss of receptive language, retained some language expressive language “wire” with a few verbs, suspected deafness child’s frustration, surprised by their own change; behaviors similar to those of autism, IQ (IQ) nonverbal normal or above average, EEG abnormalities (EEG).  Some experts suspect that some cases of childhood disintegrative disorder (CDD) or late onset of autism might actually be Landau-Kleffner syndromes.

The occurrence of the disorder is associated with paroxysmal abnormalities in the electroencephalogram (usually in the temporal lobes, usually in a bilateral, but often with a more generalized disorder disrítmico) and in most cases also of seizures. The onset usually occurs between three and seven years old, but can occur earlier or later in childhood. In a quarter of cases of language loss occurs gradually over a period of several months, but most often is that the loss is sudden, in the course of days or weeks.

The temporal relationship between onset of the attacks and loss of speech is often variable, one preceding the other or vice versa, with an interval of several months to two years. It is characteristic that the deterioration of language comprehension is profound, and that difficulties in understanding the sounds are the first manifestation of this disorder. Some children fall silent altogether, others limit their expression to a particular jargon, while others have milder deficits in the expression and verbal fluency, often accompanied by dysarthria.

In some cases it presents an impact on the quality of the vocals, with a loss of normal inflections. Sometimes in the early stages of the disorder seems to fluctuate to the affectation of speech functions. In the months after the initial loss of language are quite common behavioral disorders and emotional, but these tend to improve as the child becomes a means of communication.